char = E;code = 69
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char = p;code = 112
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char = t;code = 116
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char = t;code = 116
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char = W;code = 87
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char = e;code = 101
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char = s;code = 115
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char = .;code = 46
result sql = Endoscopic manifestations of Wegener disease.
Endoscopic manifestations of Wegener disease.
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char = h;code = 104
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char = r;code = 114
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char = p;code = 112
char = p;code = 112
char = e;code = 101
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char = a;code = 97
char = y;code = 121
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char = z;code = 122
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char = W;code = 87
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char = ';code = 39
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char = H;code = 72
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char = f;code = 102
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char = r;code = 114
char = e;code = 101
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char = a;code = 97
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char = i;code = 105
char = o;code = 111
char = n;code = 110
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char = t;code = 116
char = h;code = 104
char = ;code = 32
char = o;code = 111
char = t;code = 116
char = h;code = 104
char = e;code = 101
char = r;code = 114
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char = d;code = 100
char = i;code = 105
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char = a;code = 97
char = s;code = 115
char = e;code = 101
char = s;code = 115
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char = k;code = 107
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char = f;code = 102
char = f;code = 102
char = i;code = 105
char = c;code = 99
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char = l;code = 108
char = t;code = 116
char = .;code = 46
char = ;code = 32
char = E;code = 69
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char = a;code = 97
char = b;code = 98
char = l;code = 108
char = i;code = 105
char = s;code = 115
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char = i;code = 105
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char = g;code = 103
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char = a;code = 97
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char = e;code = 101
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char = ;code = 32
char = v;code = 118
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char = t;code = 116
char = ;code = 32
char = t;code = 116
char = o;code = 111
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char = i;code = 105
char = n;code = 110
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char = m;code = 109
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char = z;code = 122
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char = ;code = 32
char = l;code = 108
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char = s;code = 115
char = s;code = 115
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char = ;code = 32
char = f;code = 102
char = u;code = 117
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char = c;code = 99
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char = ;code = 32
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char = i;code = 105
char = c;code = 99
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char = d;code = 100
char = e;code = 101
char = f;code = 102
char = o;code = 111
char = r;code = 114
char = m;code = 109
char = i;code = 105
char = t;code = 116
char = y;code = 121
char = .;code = 46
char = ;code = 32
char = I;code = 73
char = n;code = 110
char = ;code = 32
char = t;code = 116
char = h;code = 104
char = e;code = 101
char = ;code = 32
char = l;code = 108
char = a;code = 97
char = s;code = 115
char = t;code = 116
char = ;code = 32
char = f;code = 102
char = i;code = 105
char = f;code = 102
char = t;code = 116
char = e;code = 101
char = e;code = 101
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char = y;code = 121
char = e;code = 101
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char = ,;code = 44
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char = w;code = 119
char = e;code = 101
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char = e;code = 101
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char = g;code = 103
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char = ;code = 32
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char = e;code = 101
char = s;code = 115
char = ;code = 32
char = o;code = 111
char = f;code = 102
char = ;code = 32
char = W;code = 87
char = G;code = 71
char = .;code = 46
char = ;code = 32
char = I;code = 73
char = n;code = 110
char = ;code = 32
char = s;code = 115
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char = x;code = 120
char = ;code = 32
char = p;code = 112
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char = t;code = 116
char = i;code = 105
char = e;code = 101
char = n;code = 110
char = t;code = 116
char = s;code = 115
char = ,;code = 44
char = ;code = 32
char = W;code = 87
char = G;code = 71
char = ;code = 32
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char = p;code = 112
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char = a;code = 97
char = .;code = 46
char = ;code = 32
char = O;code = 79
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char = O;code = 79
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char = o;code = 111
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char = c;code = 99
char = ;code = 32
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char = c;code = 99
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char = l;code = 108
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char = s;code = 115
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char = o;code = 111
char = f;code = 102
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char = .;code = 46
char = ;code = 32
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char = n;code = 110
char = ;code = 32
char = f;code = 102
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char = r;code = 114
char = ;code = 32
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char = e;code = 101
char = s;code = 115
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char = ;code = 32
char = s;code = 115
char = e;code = 101
char = r;code = 114
char = o;code = 111
char = l;code = 108
char = o;code = 111
char = g;code = 103
char = i;code = 105
char = c;code = 99
char = a;code = 97
char = l;code = 108
char = l;code = 108
char = y;code = 121
char = ;code = 32
char = a;code = 97
char = n;code = 110
char = t;code = 116
char = i;code = 105
char = c;code = 99
char = y;code = 121
char = t;code = 116
char = o;code = 111
char = p;code = 112
char = l;code = 108
char = a;code = 97
char = s;code = 115
char = m;code = 109
char = i;code = 105
char = c;code = 99
char = ;code = 32
char = a;code = 97
char = n;code = 110
char = t;code = 116
char = i;code = 105
char = b;code = 98
char = o;code = 111
char = d;code = 100
char = i;code = 105
char = e;code = 101
char = s;code = 115
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char = a;code = 97
char = g;code = 103
char = a;code = 97
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char = n;code = 110
char = s;code = 115
char = t;code = 116
char = ;code = 32
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char = e;code = 101
char = u;code = 117
char = t;code = 116
char = r;code = 114
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char = p;code = 112
char = h;code = 104
char = i;code = 105
char = l;code = 108
char = ;code = 32
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char = l;code = 108
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char = s;code = 115
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char = ;code = 32
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char = ;code = 32
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char = l;code = 108
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char = o;code = 111
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char = l;code = 108
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char = n;code = 110
char = i;code = 105
char = c;code = 99
char = a;code = 97
char = l;code = 108
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char = n;code = 110
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char = s;code = 115
char = t;code = 116
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char = o;code = 111
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char = c;code = 99
char = a;code = 97
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char = ;code = 32
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char = n;code = 110
char = d;code = 100
char = i;code = 105
char = n;code = 110
char = g;code = 103
char = s;code = 115
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char = ;code = 32
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char = e;code = 101
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char = n;code = 110
char = a;code = 97
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char = i;code = 105
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char = n;code = 110
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char = ;code = 32
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char = h;code = 104
char = e;code = 101
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char = e;code = 101
char = ;code = 32
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char = t;code = 116
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char = b;code = 98
char = o;code = 111
char = d;code = 100
char = i;code = 105
char = e;code = 101
char = s;code = 115
char = ;code = 32
char = g;code = 103
char = i;code = 105
char = v;code = 118
char = e;code = 101
char = ;code = 32
char = t;code = 116
char = h;code = 104
char = e;code = 101
char = ;code = 32
char = p;code = 112
char = o;code = 111
char = s;code = 115
char = s;code = 115
char = i;code = 105
char = b;code = 98
char = i;code = 105
char = l;code = 108
char = i;code = 105
char = t;code = 116
char = y;code = 121
char = ;code = 32
char = t;code = 116
char = o;code = 111
char = ;code = 32
char = s;code = 115
char = o;code = 111
char = l;code = 108
char = v;code = 118
char = e;code = 101
char = ;code = 32
char = d;code = 100
char = i;code = 105
char = f;code = 102
char = f;code = 102
char = i;code = 105
char = c;code = 99
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char = l;code = 108
char = t;code = 116
char = i;code = 105
char = e;code = 101
char = s;code = 115
char = ;code = 32
char = i;code = 105
char = n;code = 110
char = ;code = 32
char = W;code = 87
char = G;code = 71
char = ;code = 32
char = d;code = 100
char = i;code = 105
char = f;code = 102
char = f;code = 102
char = e;code = 101
char = r;code = 114
char = e;code = 101
char = n;code = 110
char = t;code = 116
char = i;code = 105
char = a;code = 97
char = l;code = 108
char = ;code = 32
char = d;code = 100
char = i;code = 105
char = a;code = 97
char = g;code = 103
char = n;code = 110
char = o;code = 111
char = s;code = 115
char = i;code = 105
char = s;code = 115
char = .;code = 46
char = <;code = 60
char = b;code = 98
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char = /;code = 47
char = >;code = 62
result sql = The diagnostic criteria for upper airway necrotizing diseases such as Wegener's granulomatosis (WG) are well defined. However, the differentiation with other diseases of unknown aetiology remains difficult. Establishing an early diagnosis and prompt treatment is very important to minimize loss of function and cosmetic deformity. In the last fifteen years, we observed and treated eight cases of WG. In six patients, WG appeared primarily in the nose area. One patient presented primarily middle ear and secondary nose involvement, whereas in one case, the inner ear was affected too. One patient did not present nasal involvement although the middle ear and several cranial nerves were involved. For these patients, the pathognomonic diagnosis had not been confirmed by biopsy at the early stage and we introduced an immunosuppressive therapy on the basis of clinical and histological findings only. For the eight patients, the treatment stopped the disease process but for one patient, we abandoned drugs because of side effects. Finally, only four of the cases only had a pathognomonic histological diagnosis of WG. In four cases, serologically anticytoplasmic antibodies against neutrophil granulocytes (Anca) were observed early. Both clinical and histological findings and determination of these antibodies give the possibility to solve difficulties in WG differential diagnosis.

Publication: Acta Otorhinolaryngol Belg 1996 ;50(3)::159-65.
Publication Date: 1996
Study Author(s): Bovy, P;Daele, J;Samain, P;
Institution: ENT Department, C.H.R. La Citadelle, Liège, Belgium.
Shortcut link to this study:
The diagnostic criteria for upper airway necrotizing diseases such as Wegener's granulomatosis (WG) are well defined. However, the differentiation with other diseases of unknown aetiology remains difficult. Establishing an early diagnosis and prompt treatment is very important to minimize loss of function and cosmetic deformity. In the last fifteen years, we observed and treated eight cases of WG. In six patients, WG appeared primarily in the nose area. One patient presented primarily middle ear and secondary nose involvement, whereas in one case, the inner ear was affected too. One patient did not present nasal involvement although the middle ear and several cranial nerves were involved. For these patients, the pathognomonic diagnosis had not been confirmed by biopsy at the early stage and we introduced an immunosuppressive therapy on the basis of clinical and histological findings only. For the eight patients, the treatment stopped the disease process but for one patient, we abandoned drugs because of side effects. Finally, only four of the cases only had a pathognomonic histological diagnosis of WG. In four cases, serologically anticytoplasmic antibodies against neutrophil granulocytes (Anca) were observed early. Both clinical and histological findings and determination of these antibodies give the possibility to solve difficulties in WG differential diagnosis.
PMID: 8888896

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